Natural Osmolyte TrimethylamineN-Oxide Corrects Assembly Defects of Mutant Branched-Chain Α-Ketoacid Decarboxylase in Maple Syrup Urine Disease

Journal of Biological Chemistry - United States
doi 10.1074/jbc.m107242200
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American Society for Biochemistry & Molecular Biology (ASBMB)

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