Accumulation of 3-Hydroxy-Fatty Acids in the Culture Medium of Long-Chain L-3-Hydroxyacyl CoA Dehydrogenase (LCHAD) and Mitochondrial Trifunctional Protein-Deficient Skin Fibroblasts: Implications for Medium Chain Triglyceride Dietary Treatment of LCHAD Deficiency
Pediatric Research - United States
doi 10.1203/01.pdr.0000059748.67987.1f
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May 1, 2003
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Springer Science and Business Media LLC